CASE REPORT
Cordoma é um tumor ósseo agressivo e raro que representa 1-4% dos tumores ósseos e afeta cerca de 0,1/100.000 pessoas/ano. Sua maior incidência está na região do clivus, sacro, e é menos comum na coluna dorsal. Seus achados clínicos são inicialmente inespecíficos. Assim, à medida que o tumor cresce, sintomas mais específicos - associados à compressão nervosa - tendem a aparecer. O melhor exame de imagem para visualização do cordoma e planejamento cirúrgico é a ressonância magnética. O diagnóstico confirmatório é feito por microscopia e, principalmente, por estudo imuno-histoquímico. O tratamento consiste principalmente na ressecção cirúrgica máxima e radiação específica. A recorrência é comum apesar destas modalidades de tratamento. Nosso estudo destaca um caso raro de cordoma torácico e o papel da remoção total como uma opção de tratamento eficaz.
Chordoma is an aggressive and rare bone tumor that represents 1-4% of bone tumors and affects about 0.1/100,000 people/year. Its highest incidence is in the region of the clivus, sacrum, and is less common in the dorsal spine. Its clinical findings are initially nonspecific. Thus, as the tumor grows, more specific symptoms - associated with nerve compression - tend to appear. The best imaging exam for visualization of the chordoma and surgical planning is magnetic resonance imaging. The confirmatory diagnosis is made by microscopy and, mainly, by immunohistochemistry study. Treatment consists mainly of maximal surgical resection and specific radiation. Recurrence is common despite these treatment modalities. Our study highlights a rare case of thoracic chordoma and the role of total removal as an effective treatment option.
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1Faculdade de Medicina Nova Esperança – FAMENE, João Pessoa, PB, Brasil.
2Universidade Federal da Paraíba – UFPB, João Pessoa, PB, Brasil.
3Hospital Metropolitano Dom José Maria Pires, Santa Rita, PB, Brasil.
4Faculdade de Ciências Médicas da Paraíba – FCM-PB, Cabedelo, PB, Brasil.
Received Mar 5, 2023
Corrected May 9, 2023
Accepted June 30, 2023