CASE REPORT
Encefaloceles são malformações que resultam em extravasamento de conteúdo intracraniano devido à ausência de sutura no crânio. Podem ocorrer nas regiões occipital, parietal temporal e frontal, sendo a região mais comumente acometida a occipital. Entre as encefaloceles existe uma forma rara denominada encefalocele gigante, que pode atingir as dimensões do crânio. As encefaloceles gigantes sempre são um desafio para os neurocirurgiões e são poucos os casos relatados na literatura. São relatados dois casos, um bebê de 25 dias com lesão lobulada com cística de grandes dimensões em região parietal, sem outras alterações nos movimentos ou no sistema nervoso central. O outro é uma criança de 9 meses com rotura de encéfalo occipital, apresentando défices neurológicos.
Encephaloceles are malformations that results in extravasation of intracranial contents due to absence of suture in the cranium. They can occur in the occipital, parietal temporal and frontal regions, and the most common region affected is the occipital. Among encephaloceles there is a rare form called Giant encephalocele, which can achieve the dimensions of the skull. Giant encephaloceles always are a challenge for Neurosurgeons and there are few cases reported in literature. Two cases are reported, one 25 day-old baby with a lobulated lesion with cystic of great dimensions in parietal region, without other alteration in the moviments or central nervous system. The other one is a 9 month-old child with ruptured occipital encephaloce, and presenting neurological deficits.
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1 Medical student, Faculty of Medicine, State University of Amazonas, Manaus (AM), Brazil.
2 Medical student, Federal University of Amazonas of Medicine, Manaus (AM), Brazil.
3 MD, Post-Graduation Program on Basic and Advanced Immunology, Federal University of Amazonas, Manaus (AM), Brazil.
4 MD, Division of Neurosurgery, Getúlio Vargas Universitary Hospital, Manaus (AM), Brazil.
Received Jan 1, 2023
Corrected Feb 15, 2023
Accepted Feb 18, 2023
