CASE REPORT

Meduloblastoma Nodular Desmoplásico Localizado no Ângulo Pontocerebelar. Relato de Caso

Desmoplastic Nodular Medulloblastoma Located at the Cerebellopontine Angle. Case Report

  • Augusto Cesar Santos Esmeraldo (1,2)
  • Ivison Xavier Duarte (3)
  • Marcos Paulo Teixeira Santos (4)
  • Carlos Umberto Pereira (5,6)
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Resumo

Introdução: o meduloblastoma é raro na idade adulta. A localização primária no ângulo pontocerebelar é pouco relatada na literatura. Relato do caso: paciente de 22 anos de idade, masculino, com história de vertigem e zumbidos associado a cefaleia. Submetido à ressonância magnética do crânio que demonstrou lesão expansiva no ângulo pontocerebelar direito. Resultado: submetido a craniectomia suboccipital direita e exérese total da lesão. Resultado do exame anatomopatológico foi de meduloblastoma nodular desmoplásico. Conclusão: devemos considerar a possibilidade de meduloblastoma no diagnóstico diferencial em lesões que envolvem o ângulo pontocerebelar.

Palavras-chave

Tumor; Ângulo pontocerebelar; Diagnóstico diferencial; Meduloblastoma; Fossa posterior

Abstract

Introduction: medulloblastoma is rare in adulthood. The primary location in the cerebellopontine angle has few reports in the literature. Case presentation: a 22-year-old male patient with a history of vertigo and tinnitus associated with headache is reported. He was submitted to magnetic resonance imaging of the skull and an expansive lesion at the right cerebellopontine angle was found. Results: right suboccipital craniectomy and total lesion excision were performed. Diagnosis was set as Desmoplastic/nodular medulloblastoma. Conclusion: we should consider the possibility of diagnosis of medulloblastoma in the differential diagnosis in lesions involving the cerebellopontine angle.

Keywords

Tumor; Cerebellopontine angle; Differential diagnosis; Medulloblastoma; Posterior fossa

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(1) MD, Head of the Neurosurgery Medical Residency, Fundação Beneficência Hospital de Cirurgia, Aracaju (SE), Brazil.

(2) Neurosurgeon, Hospital de Urgência de Sergipe – HUSE, Aracaju (SE), Brazil.

(3) MD, Pathogist, Fundação Beneficência Hospital Cirurgia, Aracaju (SE), Brazil.

(4) MD, MR, Medical Residency in Neurosurgery, Fundação Beneficência Hospital de Cirurgia, Aracaju (SE), Brazil.

(5) MD, PhD, Preceptor at Neurosurgery Service, Fundação Beneficência Hospital de Cirurgia, Aracaju (SE), Brazil.

(6) Neurosurgeon, Hospital de Urgência de Sergipe – HUSE, Aracaju (SE), Brazil.

 

Received Mar 7, 2019
Accepted Mar 31, 2022

JBNC  Brazilian Journal of Neurosurgery

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